Severe bleeding after tonsillectomy can lead to airway obstruction and be life-threatening. We report a case of post-tonsillectomy bleeding in a ten-year-old patient with previously undiagnosed hemophilia A, with a history of bleeding after circumcision and hematomas following minimal trauma. He was treated for rheumatic fever because of arthritis and repeated sore throats, for which reason he underwent tonsillectomy. In the postoperative period, the patient presented active bleeding even after ligation of the left pillars, with a prolonged APTT in the biological work-up and a factor VIII dosage that collapsed to 0. The patient was diagnosed with hemophilia A major at 7% and was treated with an anti-hemophilic factor with good improvement.
Cite this paper
Nassiri, N. , Zahiri, H. , Ghanam, A. , Ouali, A. E. , Babakhouya, A. , Rkain, M. and Benajiba, N. (2023). From Rheumatic Fever to Hemophilia a Major: A Case Report. Open Access Library Journal, 10, e9826. doi: http://dx.doi.org/10.4236/oalib.1109826.
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