Background: Neurological, cardiac, and vascular involvement in Behçet disease is very rare with higher mortality. The coexistence of manifestations in the same patient is exceptional. This makes management challenging because of the very high risk of bleeding. Case Summary: We report the case of a 25-year-old man who was admitted with an acute motor deficit in all four limbs. A thoracic angioscan showed a thrombosed aneurysm of the inferior lobar pulmonary arteries bilaterally with an obstructive intraluminal thrombus of a segmental branch of the right higher lobe. Transthoracic echocardiography (TTE) revealed a mobile right atrial thrombus measuring 13 × 10 mm. The patient was treated with methylprednisolone (1 g), cyclophosphamide, colchicine, and anticoagulation (heparin sodium at curative dose, relayed by antivitamin K). Conclusion: The outcome was satisfactory with complete resolution of the intraventricular thrombus and the aneurysm, and mild neurological sequelae.
Cite this paper
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