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Neurocirugía 2011
Malformación de Chiari tipo I en un paciente con síndrome de PolandDOI: 10.4321/S1130-14732011000600014 Keywords: chiari malformation, craniovertebral junction, poland's síndrome, syringomyelia, anomaly. Abstract: chiari malformation type i and poland's syndrome are two rare diseases and their simultaneous presentation had not been previously described in the literature. we report the case of a 27 year old male with history of poland's syndrome, who referred headache and motor impairment of the intrinsic muscles of the left hand. in a cervical spine mr a chiari i malformation with syringomyelia from c1 to t2 was found, which was treated by foramen magnum decompression, dural plasty and removal of the posterior arch of the atlas. a discussion of the embryological mechanisms that might be involved in the coexistence of these two entities is presented, emphasizing the role of para-axial mesoderm.
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