%0 Journal Article
%T Malformaci¨®n de Chiari tipo I en un paciente con s¨ªndrome de Poland
%A Alcal¨¢-Cerra
%A G.
%A Sabogal-Barrios
%A R.
%A Ni£¿o-Hern¨¢ndez
%A L.M.
%A Guti¨¦rrez-Paternina
%A J.J.
%A Moscote-Salazar
%A L.R.
%A Preciado-Mesa
%A E.
%J Neurocirug¨ªa
%D 2011
%I Scientific Electronic Library Online
%R 10.4321/S1130-14732011000600014
%X chiari malformation type i and poland's syndrome are two rare diseases and their simultaneous presentation had not been previously described in the literature. we report the case of a 27 year old male with history of poland's syndrome, who referred headache and motor impairment of the intrinsic muscles of the left hand. in a cervical spine mr a chiari i malformation with syringomyelia from c1 to t2 was found, which was treated by foramen magnum decompression, dural plasty and removal of the posterior arch of the atlas. a discussion of the embryological mechanisms that might be involved in the coexistence of these two entities is presented, emphasizing the role of para-axial mesoderm.
%K chiari malformation
%K craniovertebral junction
%K poland's s¨ªndrome
%K syringomyelia
%K anomaly.
%U http://scielo.isciii.es/scielo.php?script=sci_abstract&pid=S1130-14732011000600014&lng=en&nrm=iso&tlng=en