|
An Adolescent with Pulmonary Hypertension Secondary to Idiopathic Fibrosing Mediastinitis: Case ReportKeywords: Pulmonary hypertension is an important determinant of morbidity and mortality in many diseases , including congenital heart disease and respiratory disease. Fibrosing mediastinitis is a rare disorder caused by proliferation of acellular collagen. In fibrosing mediastinitis , clinical presentation is determined by compression to the vital mediastinal organs. Fibrosing mediastinitis may rarely lead to pulmonary veno-occlusive disease. In this case report , a 16 year old boy with pulmonary arterial hypertensio Abstract:
|