%0 Journal Article %T An Adolescent with Pulmonary Hypertension Secondary to Idiopathic Fibrosing Mediastinitis: Case Report %A Serta£¿ Hanedan Onan %A Sadettin Sezer %A Ali Baykan %A Ertu£¿rul Mavili %J Erciyes Medical Journal %D 2012 %I Aves Yayincilik %K Pulmonary hypertension is an important determinant of morbidity and mortality in many diseases %K including congenital heart disease and respiratory disease. Fibrosing mediastinitis is a rare disorder caused by proliferation of acellular collagen. In fibrosing mediastinitis %K clinical presentation is determined by compression to the vital mediastinal organs. Fibrosing mediastinitis may rarely lead to pulmonary veno-occlusive disease. In this case report %K a 16 year old boy with pulmonary arterial hypertensio %U Child, mediastinitis, pulmonary artery, pulmonary hypertension