The anesthetic management in the patient with Kabuki makeup syndrome

Kabuki makeup syndrome is characterized by mentalretardation, characteristic facial appearance (ektropion),skeletal abnormalities, joint laxity, short stature. The syndromeis thought to be a consequence of otosomal dominantmutation. Important factors in anesthetical managementof these patients include; difficult airway, cardiologicproblems, obstructive sleeps apne, hypotoni and malignshyperthermia risks. In this case report we aimed to discussanesthesic management of a patient with Kabukisyndrome -a rare clinical entity in our country- . J Clin ExpInvest 2013; 4 (1): 116-118Key words: kabuki makeup, tympanoplasty, general anesthesia