%0 Journal Article %T The anesthetic management in the patient with Kabuki makeup syndrome %A £¿smail Ayd£¿n Erden %A Ayhan K£¿seo£¿lu %A Bekir Suat K¨¹rk£¿¨¹o£¿lu %A Seda Banu Ak£¿nc£¿ %J Journal of Clinical and Experimental Investigations %D 2013 %I Association of Health Investigations %X Kabuki makeup syndrome is characterized by mentalretardation, characteristic facial appearance (ektropion),skeletal abnormalities, joint laxity, short stature. The syndromeis thought to be a consequence of otosomal dominantmutation. Important factors in anesthetical managementof these patients include; difficult airway, cardiologicproblems, obstructive sleeps apne, hypotoni and malignshyperthermia risks. In this case report we aimed to discussanesthesic management of a patient with Kabukisyndrome -a rare clinical entity in our country- . J Clin ExpInvest 2013; 4 (1): 116-118Key words: kabuki makeup, tympanoplasty, general anesthesia %K kabuki makeup %K tympanoplasty %K general anesthesia %U http://www.jceionline.org/upload/sayi/16/JCEI-00655.pdf