Hipogammaglobulinemia congénita asociada con trastornos de los granulocitos.: Presentación de un caso

this is the case of a child aged 11 months with a history of systemic sepsis from pseudomona aeruginosa at 5 months, neutropenia, leucopenia, sepsis-associated anemia and from then, recurrent acute respiratory infections of the high respiratory tract, allergic manifestations and furunculosis from pseudomona. immunologic study conducted showed a decreased figure of igg with a light increase of cd4+ cooperative-igm of t cells. also, we found the presence of neutropenia and marked defect of phagocytosis. we made the diagnosis of granulocyte-associate congenital hypogammaglobulinemia. the patient was treated with human gamma globulin by intramuscular route, transference factor and immunoferon, with an obvious improvement.