%0 Journal Article
%T Hipogammaglobulinemia cong¨¦nita asociada con trastornos de los granulocitos.: Presentaci¨®n de un caso
%A S¨¢nchez Segura
%A Miriam C.
%A Mars¨¢n Su¨¢rez
%A Vianed
%A Socarr¨¢s Ferrer
%A Bertha B.
%A Ojeda de Le¨®n
%A Norma
%A N¨²£¿ez Quintana
%A Aram¨ªs
%A Insua Arregui
%A Concepci¨®n
%A del Valle P¨¦rez
%A L¨¢zaro O.
%A Arce Hern¨¢ndez
%A Ada A.
%A Mac¨ªas Abraham
%A Consuelo
%J Revista Cubana de Hematolog£¿-a, Inmunolog£¿-a y Hemoterapia
%D 2009
%I Editorial Ciencias M¨¦dicas
%X this is the case of a child aged 11 months with a history of systemic sepsis from pseudomona aeruginosa at 5 months, neutropenia, leucopenia, sepsis-associated anemia and from then, recurrent acute respiratory infections of the high respiratory tract, allergic manifestations and furunculosis from pseudomona. immunologic study conducted showed a decreased figure of igg with a light increase of cd4+ cooperative-igm of t cells. also, we found the presence of neutropenia and marked defect of phagocytosis. we made the diagnosis of granulocyte-associate congenital hypogammaglobulinemia. the patient was treated with human gamma globulin by intramuscular route, transference factor and immunoferon, with an obvious improvement.
%K hypogammaglobulinemia
%K primary immunodeficiency
%K neutropenia
%K phagocytosis.
%U http://scielo.sld.cu/scielo.php?script=sci_abstract&pid=S0864-02892009000300010&lng=en&nrm=iso&tlng=en