Tumor intraabdominal desmoplásico de células peque？as y redondas: Revisión de la literatura a propósito de un caso con estudio citológico, histopatológico, inmunohistoquímico y molecular

purpose: to review the cyto-histopathological, immunohistochemical and molecular characteristics of small round cell desmoplastic tumor (dsrct). material and methods: a 18 year old male with an intraabdominal epigastric mass. results: the tumor consisted of nests and masses of undifferentiated small round cells embedded in a desmoplastic stroma, with areas of rosette formation immuno-reactive to cytokeratins, vimentin, desmin, enolase, and wt1 fraction of the ews/wt1 fusion protein transcript. the molecular study demonstrated the existence of the translocation t(11;22)(p13;q12). conclusions: the solid areas and rosette formation have been described in other cases of dsrct. the chimeric transcription product can be detected by rt-pcr, southern-blot, western-blot, and immunohistochemistry. cytology is especially useful in recurrences. the differential diagnosis should be made with the small round undifferented cell tumors group.