Tumor Teratóide Rabdóide Atípico Num Adulto

atypical teratoid rhabdoid tumor (at/rt) is a rare and aggressive malignancy, which is more common in early childhood and carries a poor prognosis. only 23 cases have been described in adults. a treatment strategy is yet to be established but gross total resection (gtr), early radiotherapy (rt) and platinum and alkylator-based chemotherapy seem to be associated with better outcome. we report on a 39 year-old female who presented with headache, vertigo, blurry vision and ataxia. the mri revealed hydrocephalus related to a mass at the pineal region. the treatment consisted of gtr, rt and 3 cycles of an outpatient-based ice regimen. the patient remains disease-free 30 months after diagnosis. following this case, a review of the literature is undertaken.