Enfermedad cardíaca grave en la esclerosis sistémica

a 36 year-old female with a diagnosis of systemic sclerosis suffered from an acute episode of skeletal myositis and refractory heart failure with cardiogenic shock. despite immunosuppressive treatment with high doses of corticosteroids and hemodynamic support she died five days after admission. the autopsy showed cardiac myocytolysis, myocyte necrosis and contraction band necrosis. there are very few reported cases of severe heart failure associated to systemic sclerosis.