Lúpus eritematoso sistêmico bolhoso: diagnóstico diferencial com dermatite herpetiforme

bullous systemic lupus erythematosus is a rare subset of systemic lupus erythematosus that is even rarer in pediatric patients. we report a case of a 12-year-old girl who presented with a vesiculobullous eruption on her face, neck, trunk and genital and oral mucosa, as well as anemia, sterile pyuria, ana (1:1280, speckled pattern) and positive anti-sm and anti-rnp. pathological examination suggested dermatitis herpetiformis, and direct immunofluorescence revealed igg, iga and fibrin in the epithelial basement membrane zone. we present a typical case of bullous systemic lupus erythematosus and emphasize the importance of clinical and histopathological differential diagnosis with dermatitis herpetiformis