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双眼真性小眼球继发青光眼1例
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Abstract:
真性小眼球是一种罕见的先天性遗传性眼病，是由于胚胎发育过程中胚裂闭合，眼球发育停滞所致，主要特点包括眼轴短、前房浅、房角窄、巩膜厚、视盘拥挤等，表现为高度远视，常伴弱视，容易继发青光眼，且晚期保守治疗效果不佳，需根据患者情况制定个性化手术方案。本例患者为双眼真性小眼球，继发性青光眼，并发性白内障，通过阐述该例患者临床手术治疗方案为广大眼科医生提供临床思路。
True microphthalmia is a rare congenital inherited eye disease caused by the closure of embryonic fissures during embryonic development, resulting in stagnant eye development. Its main characteristics include short axial length, shallow anterior chamber, narrow angle, thick sclera, and crowded optic disc. It is characterized by high hyperopia, often accompanied by amblyopia, and is prone to secondary glaucoma. Conservative treatment in the late stage is ineffective, and personalized surgical plans need to be developed according to the patient’s condition. The patient in this case has true microphthalmia in both eyes, secondary glaucoma, and concurrent cataracts. By elaborating on the clinical surgical treatment plan for this patient, we aim to provide clinical insights for ophthalmologists.
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