Background: Paget’s disease of the breast also called mammary Paget’s disease [MPD] was first described by Sir James Paget an English surgeon and a medical pioneer in the 19th century in 1874. In his report, fifteen women with a chronic eczematous disease on the skin of the nipple and the areola also had an associated intra ductal carcinoma of the underlying mammary gland. It is a rare type of cancer that develops in the skin of the nipple, and sometimes the areola, for this reason patients tend to take it less seriously. Conclusion: The treatment for Paget’s disease of the breast typically involves surgery, usually a mastectomy or breast conserving surgery with radiation, and effective chemotherapy or hormone therapy, depending on the underlying cancer’s characteristics.
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