Single Ventricle Type of Tricuspid Atresia with Pulmonary Stenosis in an 18-Month-Old Child in the Pediatrics Department of the Donka National Hospital/Guinea

Background: Univentricular hearts represent 0.5% - 1.5% of congenital heart defects. They are a heterogeneous group of malformations with the common feature of a single dominant ventricle. We report the case of an 18-month-old child with a single ventricle discovered following hospitalization for respiratory distress. Objective: To describe this rare and complex congenital heart disease and to draw practitioners’ attention to the importance of antenatal screening in identifying fetal congenital heart disease early. Case Presentation: This was an 18-month-old child, hospitalized on January 12, 2025, for respiratory difficulty, cyanosis, and physical asthenia in the context of fever. Echocardiography-Doppler showed a single ventricle type of tricuspid atresia with pulmonary stenosis. Conclusion: Single ventricle remains a rare pathology and difficult to manage in our resource-limited countries.