Rhabdoid tumors are aggressive soft tissue sarcomas predominantly affecting children under three years of age. While rare, cases of Atypical Teratoid/Rhabdoid Tumors (AT/RT) have been reported in adults, presenting unique challenges for treatment. This article presents a new therapeutic approach for adult AT/RT based on a case report and literature review. The case involves an adult male diagnosed with AT/RT who achieved a ten-year survival through a comprehensive treatment regimen. The approach includes surgical resection, intensive chemotherapy, and radiation therapy. The study highlights the importance of adopting an intensive chemotherapy protocol, typically used in pediatric cases, as a promising strategy for adult AT/RT management. This innovative proposal underscores the need for further research and therapeutic advancements to improve outcomes in this rare disease.
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