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原发性肝血管肉瘤伴出血1例并文献复习
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Abstract:
原发性肝血管肉瘤(primary hepatic angiosarcoma, PHA)是一种罕见的侵袭性间叶源性肝脏恶性肿瘤，其临床症状无特异性，早期诊断困难，进展快、复发率高。目前缺乏统一的标准治疗指南。现报道1例以“急性腹痛”为首发症状的PHA伴瘤内出血患者的病例资料，分享其治疗过程，并通过文献复习总结PHA的临床特点及治疗方式等，旨在提高临床医生对该病的认识，并为其临床治疗提供参考。
Primary hepatic angiosarcoma (PHA) is a rare and aggressive mesenchymal malignancy of the liver. Its clinical symptoms are non-specific, leading to challenges in early diagnosis. The disease progresses rapidly and has a high recurrence rate. Currently, there is a lack of standardized treatment guidelines. This article presents a case of PHA with intratumoral hemorrhage where “acute abdominal pain” was the initial presenting symptom, detailing the treatment process. Additionally, by reviewing relevant literature, this paper summarizes the clinical characteristics and therapeutic approaches for PHA, aiming to enhance clinicians’ understanding of the disease and provide valuable references for its management.
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