Bicuspid aortic valve (BAV) is a common congenital heart valve disease, often accompanied by aortic valve stenosis or regurgitation, infective endocarditis, and aortic diseases such as aortic dilation and dissection. This article aims to review the definition, pathogenesis and genetic basis, classification methods, clinical features and current status of research and treatment and prognosis of BAV, and provide reference for the diagnosis and treatment of BAV. The content and structure of this article are as follows: The first part introduces the definition of BAV; The second part introduces the etiology and classification methods of BAV; The third part briefly describes the clinical manifestations and diagnosis of BAV; The fourth part discusses the treatment strategies and prognosis prediction of BAV; Finally, the article summarizes and looks forward to the future research directions.
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