Kasabach-Merritt Syndrome consists of a set of signs and symptoms associated with capillary hemangioma with thrombocytopenia, which causes bleeding accompanied by petechiae, ecchymosis, and spontaneous hematomas. This present study aims to report a rare case of cervical lymphangioma (cystic hygroma) that later evolved into Kasabach-Merritt Syndrome, demonstrating the importance of systemic evaluation of veno-lymphatic malformations. Although rare, prompt diagnosis and therapy are necessary due to the high severity and potential fatality of the condition.”
References
[1]
Krakhecke, L.H.R., De Carli, J.P., De Carli, B.M.G. and Da Silva, S.O. (2014) Linfangioma de cabeça e pescoço: Levantamento de casos. Revista da Faculdade de Odontologia—UPF, 19, 212-217. https://doi.org/10.5335/rfo.v19i2.3956
[2]
Mukai, A.d.O., Zanlochi, A.G.S., Elias, C.P.F., Rolim, C.H., Baida, L.L., Tutia, P.C., et al. (2008) Hemangioendotelioma kaposiforme e síndrome de Kasabach-Merritt. Revista Paulista de Pediatria, 26, 192-196. https://doi.org/10.1590/s0103-05822008000200017
[3]
Bau, A.E.K. and Abagge, K.B. (2012) Childhood Hemangioma: Concept, Classification, Diagnosis and Therapeutic Update. Sociedade Brasileira de Pediatria.
[4]
Sosa-Rivera, A.M., Cáceres, A. and Cruz, S.A. (2019) Splenic Hemangioendothelioma in Pediatric Patients. Case Report. Revista Colombiana de Radiología, 30, 5105–5107.
[5]
Queiroz, M.N., Branco, T.G.A.C. and Ferreira, D.P. (2019) Adult Splenic Hemangioma Associated with Kasabach–Merritt Syndrome. Revista da Sociedade Brasileira de Clínica Médica, 17, 101-105.
[6]
Moura, R., Sobreira, M.L., Bertanha, M., Jaldin, R.G., Silva, M.M., Pereira, L., et al. (2014) Kasabach-Merritt Syndrome: Clinical vs. Surgical Treatment. Jornal Vascular Brasileiro, 13, 330-335. https://doi.org/10.1590/1677-5449.0102
[7]
Mello-Filho, F.V., Tone, L.G. and Kruschewsky, L.S. (2002) O uso de Picibanil (OK-432) no tratamento do linfangioma de cabeça e pescoço. Revista Brasileira de Otorrinolaringologia, 68, 552-556. https://doi.org/10.1590/s0034-72992002000400016
[8]
Li, L., Zhang, B., Wei, L. and Ma, L. (2020) Diagnosis and Treatment of Hemangiomas and Vascular Malformations: Current Status and Prospect. Chinese Journal of Dermatology, 12, 501-507.
[9]
Hall, G.W. (2001) Kasabach-Merritt Syndrome: Pathogenesis and Management. British Journal of Haematology, 112, 851-862. https://doi.org/10.1046/j.1365-2141.2001.02453.x
