Introduction:Pheochromocytoma is a rare cause of endocrine hypertension. We report the
case of an extra-adrenal pheochromocytoma discovered in the setting of an
abdominal mass. Observation: The patient was 25-year-old and presented
with headaches, excessive sweating and palpitations, followed by a sensation of
abdominal weightlessness and diastolic arterial hypertension. Abdominal computed tomography revealed a
retroperitoneal, right para-renalextra-adrenal
mass. In biology, an increase in urinary methoxylated derivatives at the
expense of normetanephrine. Conclusion: Pheochromocytoma is a rare
disease, diagnosed by measuring urinary or plasma methoxylated derivatives.
Conventional or nuclear imaging allows topographic diagnosis. Genetic studieshelps to identify other tumors.
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