Background: Congenital cystic adenomatoid malformation (CCAM)
is a congenital anomaly of lung development, accounting for approximately 25%
of congenital lung lesions. Respiratory distress often occurs during the neonatal
period, and in 80% to 85% of cases, the diagnosis is made before the age of 2
years following respiratory infections. Case Report: We report a case of MAKC diagnosed in the neonatal
period. The diagnosis was based on clinical, radiological and histological
elements. Our patient underwent surgical resection. Histological examination
confirmed the diagnosis of MAKC without any sign of malignancy. The
postoperative evolution was good. Conclusion: Clinicians and pathologists should recognize the
early discovery of MAKC in neonatal age. The clinical diagnosis strongly guided
by the radiological approach is confirmed by the pathological anatomy insofar
as the therapeutic sanction is surgical in the majority of the cases.
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