Cystic nephromas (CNs) are uncommon, benign renal neoplasms reported in
infants/young children of both genders and in adult females, concerning the
pediatric population few studies have been conducted. The diagnosis of cystic
nephroma is based on clinical signs, imaging tests, and anatomo-pathological
study. In children, CNs can appearas a
palpable abdominal mass in most of cases, hematuria or recurrent urinary
infections. They are characterized by multycystic architecture and the
exclusive presence of mature nephrogenic elements. Treatment is surgical with a
very good prognosis in most of cases. We are going to report a case of a
13-month-old girl child diagnosed with Cystic nephromas who presented to pediatric
emergency with unexplained crying episodes in order to increase clinicians
awareness about this rare tumor.
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