Ebstein’s anomaly is a rare congenital heart disease. We report a series of 4 cases of Ebstein’s anomaly discovered in adolescents. The mean age was？13.75 ± 0.96,？with？3 boys and one girl. Three were in heart failure. The EKG？showed atrial hypertrophy (1 case), right bundle branch block (1 case),？Wolff-Parkinson-White (1 case),？and？atrial fibrillation (1 case). Cardiomegaly？was present in all patients with a mean cardiothoracic index of 0.77 ± 0.03.？On echocardiography, the mean apical displacement of the tricuspid septal？leaflet was 22.5 ± 3.30？mm/m2, the Celermajer index was Grade 2 in 2 patients and Grade 4 in 2 patients. Depletive medical treatment was prescribed？to？3 patients. Anticoagulant therapy was initiated in one patient. Two are awaiting surgery. One death was recorded, it was at Grade 4 of the Celermajer index.
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