This Laubry-Pezzi syndrome is rarely seen in patients with ventricular septal
defect(VSD) combined
with aortic regurgitation.A 20-year-old
male patient presented to the Cardiothoracic and vascular surgery department with
a largeVSDwith severe aortic regurgitation
(AR). However, he was first symptomatic at 12 years of age and initially treated
by medical management with the suggestion of surgical correction. Nevertheless,
he was delayed getting surgical management due to his financial problem. This article
reported on an adult patient with Laubry-Pezzi syndrome and his surgical correction
and outcome.The association
of congenital defects VSD and AR needs to be identified and corrected in early life for better outcomes.
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