Background: Obstructed hemivagina and ipsilateral renal anomaly
(OHVIRA) syndrome is a rare congenital condition of the
female urogenital tract, presenting intraoperative challenges. We demonstrate
the utility of three dimensional intraoperative ultrasound to better delineate
anatomy and aid in optimal resection of the vaginal septum. Case: A
12-year-old female was referred to pediatric and adolescent gynecology for
irregular periods and evaluation of her gynecologic organs. Imaging studies
confirmed OHVIRA syndrome. She underwent uncomplicated vaginal septum
resection, guided by three dimensional intraoperative ultrasound. Summary
and Conclusion: Intraoperative ultrasound can better delineate challenging
anatomy. We show that three dimensional intraoperative ultrasound offers
significant advantages over traditional two dimensional ultrasound and is a
supplement to MRI, which may be helpful in complex anatomical cases like OHVIRA
syndrome.
References
[1]
Smith, N.A. and Laufer, M.R. (2007) Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome: Management and Follow-Up. Fertility and sterility, 87, 918-922. https://pubmed.ncbi.nlm.nih.gov/17320871/
https://doi.org/10.1016/j.fertnstert.2006.11.015
[2]
Han, B., Herndon, C.N., Rosen, M.P., Wang, Z.J. and Daldrup-Link, H. (2010) Uterine Didelphys Associated with Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome. Radiology Case Reports, 5, 327.
https://pubmed.ncbi.nlm.nih.gov/27307842/
https://doi.org/10.2484/rcr.v5i1.327
[3]
Shah, D.K. and Laufer, M.R. (2011) Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome with a Single Uterus. Fertility and Sterility, 96, e39-e41. https://pubmed.ncbi.nlm.nih.gov/21605855/
https://doi.org/10.1016/j.fertnstert.2011.05.013
[4]
Schlomer, B., Rodriguez, E. and Baskin, L. (2015) Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA) Syndrome Should Be Redefined as Ipsilateral Renal Anomalies: Cases of Symptomatic Atrophic and Dysplastic Kidney with Ectopic Ureter to Obstructed Hemivagina. Journal of Pediatric Urology, 11, 77-e1-6.
https://pubmed.ncbi.nlm.nih.gov/25797857/
https://doi.org/10.1016/j.jpurol.2014.12.004
[5]
Mandava, A., Prabhakar, R.R. and Smitha, S. (2012) OHVIRA Syndrome (Obstructed Hemivagina and Ipsilateral Renal Anomaly) with Uterus Didelphys, an Unusual Presentation. Journal of Pediatric and Adolescent Gynecology, 25, e23-e25.
https://pubmed.ncbi.nlm.nih.gov/22421561/
https://doi.org/10.1016/j.jpag.2011.11.004
[6]
Bajaj, S.K., Misra, R., Thukral, B.B. and Gupta, R. (2012) OHVIRA: Uterus Didelphys, Blind Hemivagina and Ipsilateral Renal Agenesis: Advantage MRI. Journal of Human Reproductive Sciences, 5, 67-70.
https://pubmed.ncbi.nlm.nih.gov/22870020/
https://doi.org/10.4103/0974-1208.97811
[7]
Breech, L.L. and Laufer, M.R. (2009) Müllerian Anomalies. Obstetrics and Gynecology Clinics of North America, 36, 47-68.
https://pubmed.ncbi.nlm.nih.gov/19344847/
https://doi.org/10.1016/j.ogc.2009.02.002
[8]
Miller, R.J. and Breech, L.L. (2008) Surgical Correction of Vaginal Anomalies. Clinical Obstetrics and Gynecology, 51, 223-236.
https://pubmed.ncbi.nlm.nih.gov/18463454/
https://doi.org/10.1097/GRF.0b013e31816d2181