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Poland Syndrome- A Rare Congenital ConditionDOI: https://doi.org/10.3329/jbcps.v36i4.38186 Keywords: Poland Syndrome, symbrachydactyly Abstract: Named after Sir Alfred Poland, Poland syndrome is a rare congenital anomaly classically characterized by the absence of unilateral chest wall muscles and sometimes ipsilateral symbrachydactyly (abnormally short and webbed fingers). The aetiology is probably a vascular disruption sequence of the subclavian arteries. In most cases, Poland Syndrome is sporadic. We report a 26 year old male patient with typical features of Poland Syndrome associated with bronchiectasis and mitral valve prolapse- a very rare association. To the best of our knowledge, this is the first documented case of a Poland Syndrome with rare association reported from Bangladesh. J Bangladesh Coll Phys Surg 2018; 36(4): 166-169
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