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-  2017 

Hemophagocytic Lymphohistiocytosis in Adults with Intraocular Involvement: Clinicopathologic Features of 3 Cases

DOI: 10.1159/000475551

Keywords: Hemophagocytic lymphohistiocytosis, Hemophagocytic syndrome, Multisystemic inflammation, Adult-onset hemophagocytosis, Uvea, Retina

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Abstract:

Hemophagocytic lymphohistiocytosis (HLH) is an infrequent inflammatory multisystemic syndrome. Only rare cases with ophthalmic involvement describing their pathologic features have been previously reported

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