全部 标题 作者
关键词 摘要

OALib Journal期刊
ISSN: 2333-9721
费用：99美元
投递稿件

查看量下载量

相关文章

更多...

左心室心肌致密化不全合并二尖瓣重度关闭不全1例报道并文献复习
Left Ventricular Noncompaction Cardiomyopathy Combined with Severe Mitral Insufficiency: A Case Report and Literature Review

DOI: 10.12677/ACRVM.2019.74010, PP. 57-63

Keywords: 左心室心肌致密化不全，心肌病，二尖瓣关闭不全
Left Ventricular Noncompaction Cardiomyopathy, Cardiomyopathy, Mitral Valve Insufficiency

Full-Text   Cite this paper   Add to My Lib

Abstract:

目的：探讨左心室心肌致密化不全(LVNC)合并心脏瓣膜疾病的诊断及治疗，提高临床对本病的认识水平。方法：总结我院收治的1例成人左心室心肌致密化不全合并二尖瓣重度关闭不全的临床资料，并结合国内外文献进行回顾复习。结果：患者系活动后心悸气喘6年入院，术前行超声心动图及心脏MRI等检查，诊断为LVNC伴二尖瓣重度关闭不全，并在全麻体外循环下二尖瓣置换术，术后恢复良好，心功能较入院前明显改善。结论：LVNC合并严重心脏瓣膜疾病临床较为少见，外科手术治疗是治疗LVNC合并心内畸形的有效方法，有利患者早期心功能的恢复。
Objective: To explore the diagnosis and treatment of left ventricular noncompaction cardiomyo-pathy (LVNC) combined with heart valve disease, and to improve the clinical understanding of this disease. Methods: To summarize the clinical data of 1 case of adult diagnosed with left ventricular noncompaction cardiomyopathy combined with severe mitral insufficiency in our hospital, and literature of domestic and foreign reports were reviewed. Results: The patient was admitted for 6 years with heart palpitate and asthma after activities before in hospital, severe mitral insufficiency with LVNC was diagnosed since the preoperative echocardiography and cardiac MRI were performed, and mitral valve replacement was performed under the general anesthesia and cardiopulmonary bypass, postoperative recovery was good and cardiac function was significantly improved compared with that before hospitalization. Conclusion: LVNC combined with severe heart valve disease is uncommon, and surgery is an effective method to treat LVNC combined with intracardiac malformation, which is beneficial for patients with early recovery of cardiac function.

References

[1]  Chin, T.K., Perloff, J.K., Williams, R.G., et al. (1990) Isolated Noncompaction of Left Ventricular Myocardium. A Study of Eight Cases. Circulation, 82, 507-513.
https://doi.org/10.1161/01.CIR.82.2.507
[2]  Grant, R.T. (1926) An Unusual Anomaly of the Coronary Vessels in the Malformed Heart of a Child. Heart, 13, 273-283.
[3]  Li, S., Yin, L.X., Li, C.M., et al. (2006) Eehoeardiographic Diagnosis of Noncompaction of Ventricular Myocardium and Its Clinical Potential. Chinese Journal of Ultrasound in Medicine, 22, 508-511.
[4]  Henderson, D.J. and Anderson, R.H. (2009) The Development and Structure of the Ventricles in the Human Heart. Pediatric Cardiology, 30, 588-596.
https://doi.org/10.1007/s00246-009-9390-9
[5]  Bennett, C.E. and Freudenberger, R. (2016) The Current Approach to Diagnosis and Management of Left Ventricular Noncompaction Cardiomyopathy: Review of the Literature. Cardiology Research and Practice, 2016, Article ID: 5172308.
https://doi.org/10.1155/2016/5172308
[6]  Towbin, J.A. (2010) Left Ventricular Noncompaction: A New Form of Heart Failure. Heart Failure Clinics, 6, 453-469.
https://doi.org/10.1016/j.hfc.2010.06.005
[7]  Towbin, J.A., Lorts, A. and Jefferies, J.L. (2015) Left Ventricular Non-Compaction Cardiomyopathy. The Lancet, 386, 813-825.
https://doi.org/10.1016/S0140-6736(14)61282-4
[8]  Ichida, F., Hamamichi, Y., Miyawaki, T., et al. (1999) Clinical Features of Isolated Noncompaction of the Ventricular Myocardium: Long-Term Clinical Course, Hemodynamic Properties, and Genetic Background. Journal of the American College of Cardiology, 34, 233-240.
[9]  Belanger, A.R., Miller, M.A., Donthireddi, U.R., et al. (2008) New Classification Scheme of Left Ventricular Noncompaction and Correlation with Ventricular Performance. American Journal of Cardiology, 102, 92-96.
https://doi.org/10.1016/j.amjcard.2008.02.107
[10]  Ouyang, P., Saarel, E., Bai, Y., et al. (2011) A de Novo Mutation in NKX2.5 Associated with Atrial Septal Defects, Ventricular Noncompaction, Syncope and Sudden Death. Clinica Chimica Acta, 412, 170-175.
https://doi.org/10.1016/j.cca.2010.09.035
[11]  Postma, A.V., van Engelen, K., van de Meerakker, J., et al. (2011) Mutations in the Sarcomere Gene MYH7 in Ebstein Anomaly. Circulation: Cardiovascular Genetics, 4, 43-50.
https://doi.org/10.1161/CIRCGENETICS.110.957985
[12]  王超, 杨炳昂, 林凌, 等. 超声心动图对心肌致密化不全的诊断价值[J]. 现代预防医学, 2011, 8(6): 1162-1165.
[13]  Weiford, B.C., Subbarao, V.D. and Mulhern, K.M. (2004) Noncompaction of the Ventricular Myocardium. Circulation, 109, 2965-2971.
https://doi.org/10.1161/01.CIR.0000132478.60674.D0
[14]  Chen, H., Zhang, W., Li, D., et al. (2009) Analysis of Ventricular Hypertrabeculation and Noncompaction Using Genetically Engineered Mouse Models. Pediatric Cardiology, 30, 626-634.
https://doi.org/10.1007/s00246-009-9406-5
[15]  St？hli, B.E., Gebhard, C., Biaggi, P., et al. (2013) Left Ventricular Non-Compaction: Prevalence in Congenital Heart Disease. International Journal of Cardiology, 167, 2477-2481.
https://doi.org/10.1016/j.ijcard.2012.05.095
[16]  Oechslin, E.N., Attenhofer Jost, C.H., Rojas, J.R., et al. (2000) Long-Term Follow-Up of 34 Adults with Isolated Left Ventricular Noncompaction: A Distinct Cardiomyopathy with Poor Prognosis. Journal of the American College of Cardiology, 36, 493-500.
https://doi.org/10.1016/S0735-1097(00)00755-5
[17]  St？llberger, C., Blazek, G., Dobias, C., et al. (2011) Frequency of Stroke and Embolism in Left Ventricular Hypertrabeculation/Noncompaction. American Journal of Cardiology, 108, 1021-1023.
https://doi.org/10.1016/j.amjcard.2011.05.039
[18]  Steffen, E.P., Joseph, B.S., Frank, W., et al. (2005) Left Ventricular Non-Compaction Insight from Cardiovascular Magnetic Resonance Imaging. Journal of the American College of Cardiology, 46, 101-105.
[19]  Jenni, R., Echslin, E.N. and van der Loo, B. (2007) Isolated Ventricular Non-Compaction of the Myocardjum in Adults. Heart, 93, 11-15.
https://doi.org/10.1136/hrt.2005.082271
[20]  Petersen, S.E., Selvanayagam, J.B., Wiesmann, F., et al. (2005) Left Ventricular Noncompaction: Insights from Cardiovascular Magnetic Resonance Imaging. Journal of the American College of Cardiology, 46, 101-105.
[21]  李欣洋, 任卫东. 左心室心肌致密化不全研究进展[J]. 中国医学影像技术, 2018, 34(11): 1716-1719.
[22]  St？llberger, C. and Finsterer, J. (2005) Left Ventricular Hypertrabeculation/Noncompaction and Stroke or Embolism. Cardiology, 103, 68-72.
https://doi.org/10.1159/000082050
[23]  任永凤, 王洲, 丁严, 等. 心肌致密化不全并房室瓣脱垂1例[J]. 中国医学影像技术, 2008(S1): 83.
[24]  齐胤尊, 马云鹏. 风湿性心脏病并心肌致密化不全行二尖瓣置换术后发生左室破裂死亡临床报告[J]. 临床误诊误治, 2016, 29(6): 59-62.

Full-Text

Contact Us

service@oalib.com

QQ:3279437679

WhatsApp +8615387084133