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左心室心肌致密化不全合并二尖瓣重度关闭不全1例报道并文献复习
Left Ventricular Noncompaction Cardiomyopathy Combined with Severe Mitral Insufficiency: A Case Report and Literature Review

DOI: 10.12677/ACRVM.2019.74010, PP. 57-63

Keywords: 左心室心肌致密化不全,心肌病,二尖瓣关闭不全
Left Ventricular Noncompaction Cardiomyopathy
, Cardiomyopathy, Mitral Valve Insufficiency

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Abstract:

目的:探讨左心室心肌致密化不全(LVNC)合并心脏瓣膜疾病的诊断及治疗,提高临床对本病的认识水平。方法:总结我院收治的1例成人左心室心肌致密化不全合并二尖瓣重度关闭不全的临床资料,并结合国内外文献进行回顾复习。结果:患者系活动后心悸气喘6年入院,术前行超声心动图及心脏MRI等检查,诊断为LVNC伴二尖瓣重度关闭不全,并在全麻体外循环下二尖瓣置换术,术后恢复良好,心功能较入院前明显改善。结论:LVNC合并严重心脏瓣膜疾病临床较为少见,外科手术治疗是治疗LVNC合并心内畸形的有效方法,有利患者早期心功能的恢复。
Objective: To explore the diagnosis and treatment of left ventricular noncompaction cardiomyo-pathy (LVNC) combined with heart valve disease, and to improve the clinical understanding of this disease. Methods: To summarize the clinical data of 1 case of adult diagnosed with left ventricular noncompaction cardiomyopathy combined with severe mitral insufficiency in our hospital, and literature of domestic and foreign reports were reviewed. Results: The patient was admitted for 6 years with heart palpitate and asthma after activities before in hospital, severe mitral insufficiency with LVNC was diagnosed since the preoperative echocardiography and cardiac MRI were performed, and mitral valve replacement was performed under the general anesthesia and cardiopulmonary bypass, postoperative recovery was good and cardiac function was significantly improved compared with that before hospitalization. Conclusion: LVNC combined with severe heart valve disease is uncommon, and surgery is an effective method to treat LVNC combined with intracardiac malformation, which is beneficial for patients with early recovery of cardiac function.

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