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-  2015 

不完全型川崎病小儿临床特征分析 Clinical Analysis of Children with Incomplete Kawasaki Disease

Keywords: 不完全型川崎病,临床特征,冠脉扩张

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Abstract:

目的:研究不完全型川崎病小儿的临床特征,以期早期诊疗,改善预后。方法:分析从2009年1月-2012年4月在武汉大学人民医院儿科收治的不完全型川崎病及典型川崎病患儿的临床资料,比较其在人口学特征、临床表现、实验室检查及治疗效果等方面的差异。结果:58例不完全型川崎病患儿与50例典型川崎病患儿相比,性别与年龄分布无明显差异。不完全型川崎病患儿诊断指标中的症状发生率如结膜充血、多形性皮疹、淋巴结肿大、手足肿胀、脱皮、唇干裂明显低于典型川崎病组患儿(P<0.01)。两组患儿疾病诊断时距起病的时间分别为(7.8±2.0)和(7.3±2.2)d(P=0.188)。实验室检查指标丙氨酸氨基转移酶、天门冬氨酸氨基转移酶、白细胞、血小板、C反应蛋白和血沉等在两组间差异无统计学意义(P>0.05)。冠脉扩张比例在不完全型川崎病组为34.5%,在典型川崎病组为22.0%(P=0.153)。丙种球蛋白治疗效果在两组中无明显差别(P=0.449)。结论:不完全型川崎病患儿主要症状发生率明显低于典型川崎病患儿,在冠脉损害以及丙种球蛋白治疗效果方面与典型川崎病患儿相比并无明显差别

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