Cor-triatriatum dexter is an extremely rare congenital
anomaly, in which right atrium is divided into 2 halves by a septum giving rise
to 3 atrial chambers. We report here a case of cor-triatriatum dexter who
presented at 3 days of life with tachypnea and did not respond to antibiotics.
Echocardiography revealed ostium secundum atrial septal defect (ASD) with right
to left flow, intact interventricular septum (IVS), severe tricuspid
regurgitation with pulmonary arterial hypertension and a membranous structure
dividing right atrium into 2 halves with good biventricular function. The
patient improved with sildenafil and anti-failure medication. This case of
cor-triatriatum dexter presenting with pulmonary hypertension, tricuspid
regurgitation and ASD added to the new spectrum of cor-triatriatum dexter.
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