Vogt-Koyanagi-Harada Syndrome With Severe Neurologic Impairment

Vogt-Koyanagi-Harada (VKH) syndrome is a rare systemic disease involving various melanocyt-containing organs with subacute chronic course. Bilateral uveitis associated with cutaneous, neurological and auditory abnormalities characterizes this syndrome. The degree of neurological symptoms may vary but they are usually mild.Here we report an unusual case with severe visual and neurological impairment such as bilateral amaurosis, recurrent status epilepticus episodes and progressive mental changes.