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Primary ciliary dyskinesiatwo cases reports

Keywords: Primary ciliary dyskinesia , kartagener's syndrome , bronchiectasia , dextrocardia

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Abstract:

(Received 22 December, 2009 ; Accepted 10 March, 2010)AbstractPrimary ciliary dyskinesia and Kartagener's syndrome are rare genetic disorders. There is a ciliary dysfunction in these disorders that cause recurrent infections in respiratory and sinus tracts associated with dextrocardia, chronic vasomotor rhinitis and dextrocardia. The aim of this paper is to report two rare cases of Primary ciliary dyskinesia, including one case of primary ciliary dyskinesia and Kartagener's syndrome for additional knowledge. J Mazand Univ Med Sci 2009; 19(73): 85-89 (Persian).

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