A Benign form of HbE/ Beta-Thalassemia

HbE/ β-thalassemia has a variable presentation with symptoms varying from a mild to severe form of thalassemia. We present a case of incidentally discovered HbE/β-thalassemia in a twenty eight year old male. He had splenomegaly, hemoglobin of 14.9 gm/dL and microcytic red cell indices. He had an HbE of 39.4%, HbF of 57.5% and HbA formed 3% of the total hemoglobin.