Enfermedad de Moya Moya: a propósito de un caso

Moya Moya disease is an idiophatic entity described for the first time in 1957 in Japan. A genetic background has been suggested for its origin. In the brain angiography we observed prominent collateral vessels in the basal ganglia, as well as narrow and tortuous brain arteries, changes which are due to a slow and progressive vascular occlusion. We have the case of a 35 year-old woman admitted with a diagnosis of intraparenquimatose hemorrhagic ictus, with ventricular drainage. Brain angiography showed a severe non-specific vascular inflammatory process causing occlusion of supraclinoideus segments in both internal carotid arteries, with multiple proximal and distal collateral vessels irrigating partially-affected regions, thus rendering an angiographic appearance of Moya Moya disease.