Myxofibrosarcoma of the maxillary sinus: a case report.

Myxofibrosarcoma, also known as myxoid variant of malignant fibrosis histiocytoma, is often located in the extremities and retroperitoneum of adult males. Its incidence in the ENT area is very low, therefore its diagnosis is often complicated. It has a high rate of local recurrence, although it has low rate of distant metastases. The only effective treatment is complete surgical resection, with little response to chemotherapy and radiotherapy. We present the case of a high-grade myxofibrosarcoma of the left maxillary sinus and nasal cavity, wich we treated with surgery and chemoradiation, but with bad clinical evolution.