Non Syndromic Oligodontia

Anodontia is a rare genetic disorder which represents the congenital absence of all teeth in primary, permanent or both dentitions. Anodontia is usually a part of a syndrome and seldom occurs as an isolated entity. It is commonly associated with complex pathology known as Ectodermal dysplasia which originates from the abnormalities during the early stages of embryonic development, and usually transmitted as an X- linked recessive disorder. In this report a case of 9 year old girl is presented who had few set of primary dentition, but surprisingly complete absence of permanent dentition except tooth buds of mandibular canine which were radiographically observed. In this case, anodontia is not associated with any syndrome which is a rare finding.