RAPUNZEL SYNDROME WITH SUPERIOR MESENTERIC ARTERY SYNDROME: A CASE REPORT AND REVIEW OF THE LITERATURE

We report a case of Rapunzel syndrome, an unusual rare gastro-intestinal trichobezoar extending into the ileum with Superior mesenteric artery syndrome in a five year old boy, presenting with a history of pain and distension of upper abdomen since four months. His parents gave history of intermittent vomiting and ingestion of hairs and threads. He was investigated with ultrasound of abdomen, barium meal and computed tomography (CT) which revealed gastrointestinal trichobezoar extending into distal ileum(Rapunzel syndrome) with Superior mesenteric artery syndrome (SMA). The patient underwent gastrotomy which revealed a trichobezoar extending into the distal ileum with SMA syndrome, confirming ourradiological diagnosis. The mode of presentation and appearance on various imaging modalities like ultrasound, Barium meal and Computed tomography are discussed.