Congenital cystic adenomatoid malformation with prenatal diagnosis:case report

Congenital cystic adenomatoid malformation is a hamartomatous malformation accepted as an embryonic differentiation anomaly characterized by replacement of normal lung parenchyma by cysts of various sizes and numbers. The primigravid presented on her 24th week with the ultrasound findings of a fetus with unilateral cyts in left lung. Thoracoamniotic shunting was inserted at a mean gestational age of 24. Patient was born due to premature rupture of membranes and preterm delivery at a mean gestational age of 25. We present a case of congenital cystic adenomatoid malformation type I in a newborn who died in twelve hours after birth and discuss about pre- and postnatal diagnostic and therapeutic possibilities. (Turk Arch Ped 2012; 47: 294-7)