Klüver-Bucy Syndrome Accompanied with Fronto-temporal Dementia

Klüver-Bucy syndrome is characterized by visual agnosia, increased sexual engagement, placidity, hyperorality, hypermetamorphosis, alterations in affection and dietary habits. A right-handed 64-year-old man is presented with Klüver-Bucy syndrome. The clinical examination, psychometric tests and radiological examinations confirmed the diagnosis of Klüver-Bucy syndrome. The results obtained from positron emission tomography (PET) and cranial magnetic resonance imaging (MRI) showed bilateral involvement of the amygdala, defined as the basic mechanism in Klüver-Bucy syndrome. In this case report, a Klüver-Bucy syndrome with fronto-temporal dementia is discussed. (Marmara Medical Journal 2012;25:153-5)