Imaging findings in an infant with congenital pulmonary venolobar syndrome (scimitar syndrome)

Congenital venolobar syndrome (CVLS) is a rare complex malformation that includes hypoplasia of the lung, partial anomalous pulmonary venous drainage and, in a quarter of patients, associated cardiac anomalies. We present the chest radiograph and multidetector CT findings in a case of congenital venolobar syndrome in an infant, and describe the history of the condition. SA JOURNAL OF RADIOLOGY February 2012