Osteopoiquilosis y síndrome de Buschke-Ollendorf: Reporte de caso y revisión de la literatura

introduction: osteopoikilosis is a rare sclerosing bone dysplasia, its diagnosis is usually incidental on radiographs showing multiple sclerotic areas in diferent bones of the skeleton. case report: this article presents a 58 year old male patient with characteristic radiographic lesions in the femur, pelvis, skull and a with cutaneous involvement treated at the hospital universitario de santander. discussion: this disease is autosomal dominant and is apparently caused by a loss of function mutation of the gene lemd3. is occasionally associated with skin lesions, which are called buschke-ollendorf syndrome as in this case. its importance lies in the possibility of confusion with metastatic tumor lesions leading to unnecessary interventions. salud uis 2011; 43 (3): 321-326