Pautas nutricionales en el ni？o fibroquístico

cystic fibrosis is the most frequent genetic disorder of autosomal recessive inheritance in caucasians. it is ordinarily manifested as chronic obstructive pulmonary disease, typical rise of chlorine in sweat, gastrointestinal and nutritional anomalies and obstructive azoospermia that cause masculine infertility. as a multi-systemic chronic progressive disease, it demands strictly controlled nutritional therapy. energy-nutritional imbalance is given by the increase of energy and protein requirements, reduction of caloric ingestion and heavy losses in feces. adequate nutritional monitoring to submit active nutritional intervention in the first phase is necessary; then, if the situation does not change, aggressive intervention based on continuos enteral feeding should be applied. these measures are aimed at favouring the body composition and improving the pulmonary condition, the puberal development and the quality of life of the patient.