Goblet cell carcinoid tumor is a rare clinical
entity which is usually diagnosed either as acute appendicitis or advanced
cancer. Its main characteristic is that the histological findings are between
those of adenocarcinoma and typical carcinoid tumor of the appendix. Goblet
cell carcinoid tumors appear almost exclusively in the appendix, and prognosis
depends mainly on the stage and the subtype of the histological classification.
We report three cases of goblet cell carcinoid tumor in the appendix with
different clinical presentation and evolution: a 60-year-old male admitted to
the emergency room with acute abdominal pain, diagnosed with acute appendicitis
and treated with laparoscopic appendectomy; a 65-year-old male undergoing right
hemicolectomy to remove a cecal adenoma, with a goblet cell carcinoid tumor
found incidentally in the surgical specimen; and a 77-year-old male with acute
appendicitis. We discuss the main pathological and clinical findings, and
propose a set of guidelines for clinical practice.
Cite this paper
Alvarez-Laso, C. , Azcano, E. , Carrion, J. F. , Rodríguez, D. and Riera, J. R. (2017). Goblet Cell Carcinoid Tumors of the Appendix: A Report of Two Cases, Review of a Rare Clinical Entity, and Guidelines for Treatment. Open Access Library Journal, 4, e3256. doi: http://dx.doi.org/10.4236/oalib.1103256.
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