We report the case of a major neonatal form of
Crouzon syndrome of ophthalmic finding in a new- born of 21 days of age with no
background of consanguinity. The clinical manifestations were marked by signs
of Crouzon syndrome associated with dyspnea. The skull radiograph showed a
decline of maxillary and closing sutures. The brain scan was marked by a
bilateral fronto-parietal hypotrophy with agnenesis of the left
temporal. She had received a lateral tarsorrhaphy in prevention to keratopathy
of exposure. We noted a substantive consideration of normal eye and no
recurrence throttle of eyeball 6 months after tarsorrhaphy. The major forms of
Crouzon syndrome is a source of complications including exposure keratopathy
and optic atrophy requiring ophthalmological caring in awaiting for a
craniofacial surgery.
Cite this paper
Maneh, N. , Banla, M. , Douti, N. K. , Yayehd, K. , Arsene, S. , Vonor, K. , Saa, K. B. N. , Ayena, K. D. and Balo, K. P. (2014). Early Ophthalmological Manifestations of Crouzon Syndrome: About a Case. Open Access Library Journal, 1, e1046. doi: http://dx.doi.org/10.4236/oalib.1101046.
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