Background: Total situs inversus, (also called situs
transversus or oppositus) known as mirror image dextrocardia, is characterized
by a heart on the right side of the midline while the liver is on the left
side. Situs Inversus Totalis (SIT) is a congenital anomaly characterized by
complete transposition of abdominal and thoracic organs. Patients with this
anomaly usually lead a normal life. We report a fourteen-year old Nigerian who
was found to have dextrocardia with situs inversus totalis while presenting for
treatment for a different problem. Conclusion: Situs inversus totalis is a rare
finding. This report underscores the need for routine screening of children so
that such congenital anomalies can be identified and complications that follow
it averted timely.
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