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Intramural ureteric calcification in dermatomyositis mimicking pelviureteric junction obstruction

Keywords: Dermatomyositis , ureteric calcification , pelviureteric junction obstruction

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Abstract:

Juvenile dermatomyositis classically manifests as necrotising vasculitis in multiple organs. It mainly involves the vessels of skin and muscle and is associated with subcutaneous deposits of calcium. Ureteric involvement in dermatomyositis is extremely rare. The authors present a case of a 14-year-old girl with juvenile dermatomyositis with intramural ureteric calcification mimicking pelviureteric junction (PUJ) obstruction.

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