Síndrome de Gorlin-Goltz: Serie de 7 casos

nevoid basal cell carcinoma syndrome (nbcss) or gorlin-goltz syndrome is an autosomal dominant disorder principally characterized by cutaneous basal cell carcinomas, multiple keratocysts and skeletal anomalies. this report reviews current knowledge of this disorder that is important to us as specialists. the authors reviewed seven case files from the department of oral and maxillofacial surgery of h. u. la princesa from 1992-2008. the average follow up was 10 years; we determine the frequency of the clinical features and treatment in our series of nbccs.