%0 Journal Article %T Sirenomelia associada a defeitos cong¨ºnitos raros: relato de tr¨ºs casos %A Lima %A Maria Ang¨¦lica F. D. %A Machado %A Heloisa Novaes %A Dock %A Dione Correa de Ara¨²jo %A Villar %A Maria Auxiliadora Monteiro %A Llerena Junior %A Juan Clinton %J Jornal Brasileiro de Patologia e Medicina Laboratorial %D 2012 %I Sociedade Brasileira de Patologia Cl¨ªnica %R 10.1590/S1676-24442012000400010 %X sirenomelia, an extremely rare congenital defect, is defined as a limb abnormality in which the normally paired lower limbs are replaced by a single midline limb. it is commonly associated with varied genitourinary anomalies. we report three cases of sirenomelia including x-ray documentation of the lower limb. other associated aspects, whose diagnoses were established exclusively through autopsy, included bilateral renal, ureteral and bladder agenesis, rectal atresia, imperforate anus, intra-abdominal testis, absence of external genitalia and other rare congenital abnormalities. %K sirenomelia %K malformation %K pathology. %U http://www.scielo.br/scielo.php?script=sci_abstract&pid=S1676-24442012000400010&lng=en&nrm=iso&tlng=en